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Case Report

Lupus Cystitis in Association with Severe Gastrointestinal Manifestations in an Adolescent

PAUL DANCEY, EVELYN CONSTANTIN, CIARÁN M. DUFFY, and ROSIE SCUCCIMARRI

ABSTRACT.

Lupus cystitis is a rare interstitial inflammatory disease of the bladder seen in systemic lupus erythematosus that usually occurs in association with gastrointestinal manifestations, and occasionally with central nervous system involvement. There are few reported pediatric cases. We describe this entity as the presenting manifestations of lupus in an adolescent female. (J Rheumatol 2005; 32:178-80)

Key Indexing Terms:

SYSTEMIC LUPUS ERYTHEMATOSUS
INTERSTITIAL CYSTITIS
BOWEL EDEMA
ADOLESCENT


From the Division of Rheumatology, Montreal Children's Hospital, McGill University Health Center and McGill University, Montreal, Quebec, Canada.

Dr. Dancey is a Clinical Fellow of The Arthritis Society. Dr. Duffy is former Senior Research Scholar of The Arthritis Society and currently holds the Sessenwein Research Award of the Department of Pediatrics, McGill University.

P. Dancey, MD, FRCPC, Clinical Fellow, Division of Rheumatology, Department of Pediatrics, Montreal Children's Hospital; E. Constantin, MD, Pediatric Resident, Department of Pediatrics, Montreal Children's Hospital; C.M. Duffy, MB, BCh, MSc, FRCPC, Associate Professor, Director, Division of Rheumatology, Department of Pediatrics, Montreal Children's Hospital, Department of Pediatrics, McGill University; R. Scuccimarri, MD, FRCPC, Assistant Professor, Division of Rheumatology, Department of Pediatrics, Montreal Children's Hospital and McGill University.

Address reprint requests to Dr. R. Scuccimarri, Division of Rheumatology, Montreal Children's Hospital, 2300 Tupper Street, Room C-503, Montreal, Quebec H3H 1P3, Canada. E-mail:rosie.scuccimarri@muhc.mcgill.ca

Submitted February 4, 2004; revision accepted July 5, 2004.




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